??<<?>>????
??
????
??
??
]??
???
??
?????????^?????????????????????????????????????,,?,,?????.
??????.?????????,??,???(179-4).??.
Friedreich????.????.???9??.5~15???,????.?.????.??,??(??)??.,???.?-???(Bassen-Kornzweig?,?E??)Refsum(?-16)Friedreich???,?????.
???30~50?,????.??.????.
????(?),??.???????,????,?,??????.???,???,????.?Menzel?(????)Dejerine-Thomas????(????)????(Machado-Joseph)?????(Shy-Drager?).
????,T?-????(147),???.??,?,????,??.???,DNA??,???(ragged red fibers).
??
?
??
????
??
??
]??
???
??
?????????^?????????????????????????????????????,,?,,?????.
??????.?????????,??,???(179-4).??.
Friedreich????.????.???9??.5~15???,????.?.????.??,??(??)??.,???.?-???(Bassen-Kornzweig?,?E??)Refsum(?-16)Friedreich???,?????.
???30~50?,????.??.????.
????(?),??.???????,????,?,??????.???,???,????.?Menzel?(????)Dejerine-Thomas????(????)????(Machado-Joseph)?????(Shy-Drager?).
????,T?-????(147),???.??,?,????,??.???,DNA??,???(ragged red fibers).
??
?
??
“??<<?>>????” 的相关文章
????????
??????????1/5????????????????????????????
????????????????????????
??????????????
?????
?????????????? ?
?????????
??????????????????
??????
??
???
??????????
????????? ????
??
1??
2??
3??
4???
5??
????
?????????????????
?????
??????????????????????????????????
?
1
????8--1...
????????????????????????
??????????????
?????
?????????????? ?
?????????
??????????????????
??????
??
???
??????????
????????? ????
??
1??
2??
3??
4???
5??
????
?????????????????
?????
??????????????????????????????????
?
1
????8--1...
??????
????---?
?????
???????????????
?????????
??????????????????
??????
??
??????,??,??????????
??????????????
??
1??
2??
3??
4???
5??
????
?????????????????
??????
??????????????????????????
????????
?
1
????8--10?
2?
???????
3?
???????????
??
1?
???????????
2??
???????...
?????
???????????????
?????????
??????????????????
??????
??
??????,??,??????????
??????????????
??
1??
2??
3??
4???
5??
????
?????????????????
??????
??????????????????????????
????????
?
1
????8--10?
2?
???????
3?
???????????
??
1?
???????????
2??
???????...
?1??????2?????????
1.????????
?????
??
2.??????S
?
?????
??
2.??????S
?
??????
??????????
???????????
?CTY??????????????????????????
?????????????????????
???medial tarsal artery?2-3???????
? lateral tarsal artery????????????
arcuate artery???????????????????2-4????????????2-5????????????????
???first dorsal metatorsal arteries???????????????????????????????2??
?deep p...
???????????
?CTY??????????????????????????
?????????????????????
???medial tarsal artery?2-3???????
? lateral tarsal artery????????????
arcuate artery???????????????????2-4????????????2-5????????????????
???first dorsal metatorsal arteries???????????????????????????????2??
?deep p...
.????
????????????????p??????????????
???????????????????????????????????k?????????????????????????????????????????????????????????????????????????????????????????????????????13?????????????1????????????????????????????????23???????
????????????????????
???????????????????
???????????????????????????????????k?????????????????????????????????????????????????????????????????????????????????????????????????????13?????????????1????????????????????????????????23???????
????????????????????
???????????????????