??? ?
?????
(1)????????????70%75%????
(2)??????????????????????????
(3)?????????20?????10%???????????4???1????????????????????
??LD507060mg/kg(?)7340mg/kg(??)LC5037620mg/m310?() 4.3mg/L50??????2.6mg/L39????????58g/gk??3g/kg
?????10.2g/(kg)12???
??^?20?80?????????3060min8090???????????????????????????????????????????????????????????????????????????????????????
?????????????????????????????
????500mg???????15mg/24???
????(TDL0)7.5g/kg(9)??
??(TDL0)340mg/kg(57?)?
?-?? ???????????????????????????
?...
(1)????????????70%75%????
(2)??????????????????????????
(3)?????????20?????10%???????????4???1????????????????????
??LD507060mg/kg(?)7340mg/kg(??)LC5037620mg/m310?() 4.3mg/L50??????2.6mg/L39????????58g/gk??3g/kg
?????10.2g/(kg)12???
??^?20?80?????????3060min8090???????????????????????????????????????????????????????????????????????????????????????
?????????????????????????????
????500mg???????15mg/24???
????(TDL0)7.5g/kg(9)??
??(TDL0)340mg/kg(57?)?
?-?? ???????????????????????????
?...
“??? ?” 的相关文章
??
???????,,?,,?????.
??????.?????????,??,???.??.
Friedreich????.????.???9??.5~15???,????.?.????.??,??(??)??.,???.?-???(Bassen-Kornzweig?,?E??)RefsumFriedreich???,?????.
???30~50?,????.??.????.
????(?),??.???????,????,?,??????.???,???,????.?Menzel?(????)Dejerine-Thomas????(????)????(Machado-Joseph)????...
??????.?????????,??,???.??.
Friedreich????.????.???9??.5~15???,????.?.????.??,??(??)??.,???.?-???(Bassen-Kornzweig?,?E??)RefsumFriedreich???,?????.
???30~50?,????.??.????.
????(?),??.???????,????,?,??????.???,???,????.?Menzel?(????)Dejerine-Thomas????(????)????(Machado-Joseph)????...
???
1????200~990mg/L??????????????
2?????1000~2999/L????????
3???3000mg/L????????????T???-???????????????????????????????????????
???????
2?????1000~2999/L????????
3???3000mg/L????????????T???-???????????????????????????????????????
???????
?????
???????????????????????????????????????????
?????????????????o??????
????
?????????????????????g???????x??\"??\"???(???)????????(CPK)??????CPK???????
?
???????????????????????????
??
??????????????????????@??????????????
????
????????????????????
]??
??????????????????????????
?????????????????o??????
????
?????????????????????g???????x??\"??\"???(???)????????(CPK)??????CPK???????
?
???????????????????????????
??
??????????????????????@??????????????
????
????????????????????
]??
??????????????????????????
???
? ??????????????????????????? ? ??????????????? ??? ???????????? ????X-????????Duchenne?Becker 1Duchenne??DMD?????????50%??2-8?????????????????????????????Gower??????? 2Becker?BMD???????10?????????????2525???30-40????? ?????g??????????????????????????????????? ??????????????????????? ?????????-???? ...
??
????
?????????????????????????????????????????????
????????????????????o????????????2000?????????????
????
????????????????????????g???????x??"??"???(???)????????(CPK)??????CPK???????
1988?180151?83.9%?29?16.1%48?3??????????84.9%???????????19.5%15.1%
?
??4????1991108???????...
?????????????????????????????????????????????
????????????????????o????????????2000?????????????
????
????????????????????????g???????x??"??"???(???)????????(CPK)??????CPK???????
1988?180151?83.9%?29?16.1%48?3??????????84.9%???????????19.5%15.1%
?
??4????1991108???????...