??

?aortic dissection????????????????????aortic dissecting aneurysm?????aortic dissectin ghematoma??

????????????????????aortic dissecting aneurysm?????aortic dissecting hematoma????????????????????????????????????????????????????0?????????????????

??
?aortic dissection????????????????????aortic dissecting aneurysm?????aortic dissectin ghematoma??

80%?????????????????????????????????????????????????????????????????????Turner??-Ehlers-Danlos????????????????
?????66.7kPa(500mmHg)???????????????????????????????????

?????????????
?????????p?????????????????????????

?----------
??????????????????????????????^??????5?45%70%
??????????????????
?????????????????????1????????100120mmHg???6075mmHg.??????
?????????
??/????????????????
?-----------------
?3?????1???????????????????????????????????????????????????(??)???????????????1???????????????
??(1)????????...