???????
???(progressive muscula dystrophyPMD)?????????????????????????????294????
???????????????????????????
?????
???(Duchenne)
Duchenne (1868)?????????l3 00014 000(?)l22 000(?)_????????????????????????g????????????????????p???Gowers?????????????90????x????????????30??????????????15????2530??????????????(Becker)Becker(1957)?525?????1520???3610??
?(Erb)
??????1020??????????????????????????10??????
--(Landotlry-Dejerine)
????????040510????20????????????g??????????????x????????
??(Gower)
Gower?(1902)...
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