????
???Marfan\'s Syndrome???????????????????????????????????????????????????????0.04?0.1?
????????1896Marfan1?5????????1914Boerger???????1931Weve????????????????????V??????????????FBN1??????15q21.1???350KD??3??????????????????????????????????? ?????10%Reye???????????????????
[?]????? 1.??????????????????????????????????????????????????
2.??????????????
3.????80%???????????????????????????????????????
1996?????????????????????????????????????????????
[?]???8?? ?
???
?/???W/???1.05
??
20...
????????1896Marfan1?5????????1914Boerger???????1931Weve????????????????????V??????????????FBN1??????15q21.1???350KD??3??????????????????????????????????? ?????10%Reye???????????????????
[?]????? 1.??????????????????????????????????????????????????
2.??????????????
3.????80%???????????????????????????????????????
1996?????????????????????????????????????????????
[?]???8?? ?
???
?/???W/???1.05
??
20...
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